| Structural basis for activation of the titin kinase domain during myofibrillogenesis O Mayans, PFM van der Ven, M Wilm, A Mues, P Young, DO Fürst, ... Nature 395 (6705), 863-869, 1998 | 468 | 1998 |
| A mutation in the dimerization domain of filamin c causes a novel type of autosomal dominant myofibrillar myopathy M Vorgerd, PFM Van der Ven, V Bruchertseifer, T Löwe, RA Kley, ... The American Journal of Human Genetics 77 (2), 297-304, 2005 | 322 | 2005 |
| Mutations in the human muscle LIM protein gene in families with hypertrophic cardiomyopathy C Geier, A Perrot, C Özcelik, P Binner, D Counsell, K Hoffmann, B Pilz, ... Circulation 107 (10), 1390-1395, 2003 | 314 | 2003 |
| Cellular mechanotransduction relies on tension-induced and chaperone-assisted autophagy A Ulbricht, FJ Eppler, VE Tapia, PFM van der Ven, N Hampe, N Hersch, ... Current Biology 23 (5), 430-435, 2013 | 304 | 2013 |
| The structure of the sarcomeric M band: localization of defined domains of myomesin, M-protein, and the 250-kD carboxy-terminal region of titin by immunoelectron microscopy. WM Obermann, M Gautel, F Steiner, PF Van der Ven, K Weber, DO Fürst The Journal of cell biology 134 (6), 1441-1453, 1996 | 266 | 1996 |
| Indications for a novel muscular dystrophy pathway: γ-filamin, the muscle-specific filamin isoform, interacts with myotilin PFM van der Ven, S Wiesner, P Salmikangas, D Auerbach, M Himmel, ... The Journal of cell biology 151 (2), 235-248, 2000 | 232 | 2000 |
| Two immunoglobulin-like domains of the Z-disc portion of titin interact in a conformation-dependent way with telethonin A Mues, PFM van der Ven, P Young, DO Fürst, M Gautel FEBS letters 428 (1-2), 111-114, 1998 | 200 | 1998 |
| Myotilin, the limb-girdle muscular dystrophy 1A (LGMD1A) protein, cross-links actin filaments and controls sarcomere assembly P Salmikangas, PFM van der Ven, M Lalowski, A Taivainen, F Zhao, ... Human molecular genetics 12 (2), 189-203, 2003 | 193 | 2003 |
| Transient association of titin and myosin with microtubules in nascent myofibrils directed by the MURF2 RING-finger protein V Pizon, A Iakovenko, PFM Van Der Ven, R Kelly, C Fatu, DO Fürst, ... Journal of cell science 115 (23), 4469-4482, 2002 | 188 | 2002 |
| Characterization of muscle filamin isoforms suggests a possible role of γ‐filamin/ABP‐L in sarcomeric Z‐disc formation PFM van der Ven, WMJ Obermann, B Lemke, M Gautel, K Weber, ... Cell motility and the cytoskeleton 45 (2), 149-162, 2000 | 185 | 2000 |
| Clinical and morphological phenotype of the filamin myopathy: a study of 31 German patients RA Kley, Y Hellenbroich, PFM Van der Ven, DO Fürst, A Huebner, ... Brain 130 (12), 3250-3264, 2007 | 159 | 2007 |
| Mutations in the N-terminal actin-binding domain of filamin C cause a distal myopathy RM Duff, V Tay, P Hackman, G Ravenscroft, C McLean, P Kennedy, ... The American Journal of Human Genetics 88 (6), 729-740, 2011 | 146 | 2011 |
| A functional knock-out of titin results in defective myofibril assembly PFM van der Ven, JW Bartsch, M Gautel, H Jockusch, DO Fürst Journal of Cell Science 113 (8), 1405-1414, 2000 | 139 | 2000 |
| Filamin C-related myopathies: pathology and mechanisms DO Fürst, LG Goldfarb, RA Kley, M Vorgerd, M Olivé, PFM van der Ven Acta neuropathologica 125, 33-46, 2013 | 133 | 2013 |
| On noxious desmin: functional effects of a novel heterozygous desmin insertion mutation on the extrasarcomeric desmin cytoskeleton and mitochondria R Schröder, B Goudeau, MC Simon, D Fischer, T Eggermann, CS Clemen, ... Human molecular genetics 12 (6), 657-669, 2003 | 122 | 2003 |
| Disorganization of the desmin cytoskeleton and mitochondrial dysfunction in plectin-related epidermolysis bullosa simplex with muscular dystrophy R Schröder, WS Kunz, F Rouan, E Pfendner, K Tolksdorf, K Kappes-Horn, ... Journal of Neuropathology & Experimental Neurology 61 (6), 520-530, 2002 | 121 | 2002 |
| Unusual splicing events result in distinct Xin isoforms that associate differentially with filamin c and Mena/VASP PFM van der Ven, E Ehler, P Vakeel, S Eulitz, JA Schenk, H Milting, ... Experimental cell research 312 (11), 2154-2167, 2006 | 115 | 2006 |
| Xin repeats define a novel actin-binding motif D Pacholsky, P Vakeel, M Himmel, T Löwe, T Stradal, K Rottner, ... Journal of cell science 117 (22), 5257-5268, 2004 | 105 | 2004 |
| Titin and diaphragm dysfunction in chronic obstructive pulmonary disease CAC Ottenheijm, LMA Heunks, T Hafmans, PFM Van Der Ven, C Benoist, ... American journal of respiratory and critical care medicine 173 (5), 527-534, 2006 | 102 | 2006 |
| The limits of promiscuity: isoform-specific dimerization of filamins M Himmel, PFM Van Der Ven, W Stöcklein, DO Fürst Biochemistry 42 (2), 430-439, 2003 | 95 | 2003 |
